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Oral rehabilitation in a pediatric patient with hypohidrotic ectodermal dysplasia

Marcelo Mendes Pinto, Ligia Bio Razori da Silva, Thays Almeida Alfaya, Carolina Carvalho Bortoletto, Lara Jansiski Motta, Raquel Agnelli Mesquita-Ferrari, Kristianne Porta Santos Fernandes, Sandra Kalil Bussadori

Med Sci Tech 2012; 53(3): CR149-152

ID: 883615

Background:    Hypohidrotic ectodermal dysplasia is a hereditary congenital disease that affects structures of the ectoderm, such as hair, nails, skin, and sweat glands. When this condition affects dental structures, teeth may be either cone-shaped or absent.
    Case Report:    This paper describes the oral rehabilitation of a male patient aged 2 years 9 months with hypohidrotic ectodermal dysplasia who visited the dental outpatient clinic of the Universidade Nove de Julho (Sao Paulo, Brazil). The clinical and radiographic exams revealed hypodontia in several deciduous maxillary teeth, morphological alterations in deciduous teeth #51 and #61, which exhibited a cone shape, as well as anodontia of the deciduous mandibular teeth and all permanent teeth. Rehabilitation consisted of the fabrication of 2 complete crowns in indirect resin composite on the conical incisors and complete lower and partial upper dentures for the establishment of function, with the placement of an expander screw and removable Hawley appliance.
    Conclusions:    Oral rehabilitation in pediatric patients with ectodermal dysplasia is fundamental to the establishment of function, esthetics, facial contour, and psychological and social wellbeing.

Keywords: Ectodermal Dysplasia, Child, Therapeutics

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